Fatal pneumococcal septicaemia associated with asplenia and isomerism of the right atrial appendages.
نویسندگان
چکیده
A 22 month old male infant with isomerism of the right atrial appendages (associated with a complete atrioventricular septal defect, double outlet right ventricle, and pulmonary valve stenosis) died from pneumococcal septicaemia after a 36 hour illness. He had not been given penicillin prophylaxis. Asplenia was confirmed at necropsy. In a survey of 50 paediatric cardiologists in the United Kingdom, 13 (33%) of the 40 (80%) who replied did not advise any prophylactic measures against pneumococcal infection in patients with isomerism of the right atrial appendages.
منابع مشابه
معرفی یک مورد سایتوس آمبیگوس، ایزومریسم راست
When abdominal and thorasic organs are inversed it is called situs inversus and when most of the these organs are positioned abnormally and heterogenic It is called situs ambigus (Heterotoxy syndrome) which is a rare congenital defect (Incidence 1.44 in 100/000 live birth) In these, abnormal organs shift which could be to the Right side or left side (Right Isomerism, Left Isomerism). One of the...
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متن کاملMorphological considerations pertaining to recognition of atrial isomerism. Consequences for sequential chamber localisation.
The atrial morphology and venous connections were assessed "blind" in 51 necropsy specimens from patients with visceral heterotaxy. This was compared with bronchial morphology as established by dissection. Six specimens were found to have both atria and bronchi in situs solitus or inversus, and were rejected. In the remainder, atrial isomerism was diagnosed, though this required minor revision ...
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ورودعنوان ژورنال:
- British heart journal
دوره 65 2 شماره
صفحات -
تاریخ انتشار 1991